Haemophilia

Haemophilia

Why it Matters? 

Haemophilia is a rare inherited bleeding disorder caused by deficiency of clotting factors. India has only 20% diagnosed cases due to low awareness and limited facilities. Prophylaxis, regular clotting factor replacement, is a modern approach to prevent bleeds, joint damage, and disability, improving quality of life. 

 What You Should Know? 

  • Haemophilia is a rare, inherited bleeding disorder caused by deficiency or absence of clotting factors. 

  • Its symptoms include prolonged bleeding, spontaneous internal bleeding in joints/muscles, easy bruising. 

  • Untreated bleeds can cause permanent joint damage, disability, or life-threatening haemorrhage. 

  • Haemophilia is included in the National Rare Diseases Policy 2021 for improved access to treatment. 

  • Haemophilia A is caused by deficiency or absence of Factor VIII (clotting factor). 

  • Accounts for ~80–85% of all haemophilia cases worldwide. 

  • Haemophilia B is caused by deficiency or absence of Factor IX (clotting factor). 

  • Accounts for ~15–20% of haemophilia cases. 

  • Also called Christmas Disease.  

  • Its Global prevalence is ~1 in 10,000 people. 

  • Estimated Indian cases are 1–1.5 lakh, but only ~29,000 diagnosed (~20%). 

  • India has the second-highest number of haemophilia cases after the US